Wunderlich's syndrome with hepatic angiomyolipoma in tuberous sclerosis.

نویسندگان

  • R Mongha
  • P Bansal
  • A Dutta
  • R K Das
  • A K Kundu
چکیده

We present a patient of tuberous sclerosis complex with bilateral renal angiomyolipoma and hepatic angiomyolipoma with spontaneous retroperitoneal hemorrhage from right angiomyolipoma (Wunderlich's syndrome). Nephron preserving approach was tried but the right kidney could not be salvaged. Hepatic angiomyolipoma was managed conservatively. Wunderlich's syndrome has been found in around 10% of cases of renal angiomyolipomas. Hepatic Angiomyolipoma is a benign mesenchymal neoplasm of the liver which is rarely reported in literature.

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منابع مشابه

Wunderlich’s Syndrome, or Spontaneous Retroperitoneal Hemorrhage, in a Patient with Tuberous Sclerosis and Bilateral Renal Angiomyolipoma

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عنوان ژورنال:
  • Indian journal of cancer

دوره 45 2  شماره 

صفحات  -

تاریخ انتشار 2008